Esclerodermia y cirrosis biliar primaria (Síndrome de Reynolds): Descripción de un caso

[Esclerodermia y cirrosis biliar primaria (Síndrome de Reynolds): Descripción de un caso]

Merly Montenegro-Polo1, Carlos Llanos-Florez1, Andrés Mier-Beleño1, Sily Maestre-Zabala1, Ronald Maestre Serrano1, Carlos Barrera Guarín1

1. Universidad Libre Seccional Barranquilla, Facultad de Ciencias de la Salud. Km 7 Antigua vía Puerto Colombia. AA 1752, Barranquilla (Colombia).

Publicado: 2019-04-30

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Resumen

[Scleroderma and Primary Biliary Cirrhosis (Reynolds syndrome): Case Description]

RESUMEN:

El síndrome de Reynolds, se define como cirrosis biliar primaria en pacientes con esclerodermia; este sindrome debe ser sospechado en aquellos pacientes que desarrollen un patrón colestásico. Se reporta el caso de una paciente con antecedente de esclerodermia que consulta por cuadro de ictericia y a quien se le realiza estudios inmunológicos y confirmación histopatológica hepática con diagnóstico de cirrosis biliar primaria. Se ordena acido ursodesoxicólico 15mg/día por especialidades tratantes.

 

 

 

  ABSTRACT
Reynolds syndrome is defined as primary biliary cirrhosis in patients with scleroderma; this sindorme should be suspected in those patients who develop a cholestatic pattern. We report the case of a patient with a history of scleroderma who consulted due to jaundice and who underwent immunological studies and liver histopathological confirmation with a diagnosis of primary biliary cirrhosis. Ursodeoxycholic acid 15mg / day is ordered by treating specialties

 


 

 

Abstract

[Scleroderma and Primary Biliary Cirrhosis (Reynolds syndrome): Case Description]

RESUMEN:

El síndrome de Reynolds, se define como cirrosis biliar primaria en pacientes con esclerodermia; este sindrome debe ser sospechado en aquellos pacientes que desarrollen un patrón colestásico. Se reporta el caso de una paciente con antecedente de esclerodermia que consulta por cuadro de ictericia y a quien se le realiza estudios inmunológicos y confirmación histopatológica hepática con diagnóstico de cirrosis biliar primaria. Se ordena acido ursodesoxicólico 15mg/día por especialidades tratantes.

 

 

 

  ABSTRACT
Reynolds syndrome is defined as primary biliary cirrhosis in patients with scleroderma; this sindorme should be suspected in those patients who develop a cholestatic pattern. We report the case of a patient with a history of scleroderma who consulted due to jaundice and who underwent immunological studies and liver histopathological confirmation with a diagnosis of primary biliary cirrhosis. Ursodeoxycholic acid 15mg / day is ordered by treating specialties

 


 

 

Citas

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